PTU - Polskie Towarzystwo Urologiczne
list of articles:

Radical treatment of clinically malignant bladder pheochromocytoma
Article published in Urologia Polska 2005/58/4.

authors

Krzysztof Bar 1, Robert Klijer 1, Elżbieta Czekajska-Chehab 3, Waldemar Białek 1, Jerzy Michalak 1, Lech Wronecki 2
1 Katedra i Klinika Urologii Akademii Medycznej w Lublinie
Kierownik: prof. AM dr hab. Krzysztof Bar
2 Katedra i Zakład Patomorfologii Klinicznej Akademii Medycznej w Lublinie
Kierownik: prof. dr hab. Elżbieta Korobowicz
3 Zakład Radiologii Lekarskiej AM w Lublinie
Kierownik zakładu: prof. dr hab. Andrzej Drop

keywords

urinary bladder, malignant tumour, pheochromocytoma

summary

Bladder pheochromocytomas (pheochromocytoma, paraganglioma) are tumours arising from chromaffin cells in sympathetic ganglia. Most of paragangliomas are located in the adrenal medulla, while extra-adrenal localization is reported in about 10% cases. Pheochromocytoma of the urinary bladder is rare, accounting less than 0.06% of all bladder tumors. Bladder pheochromocytomas are mostly benign tumours so partial cystectomy with adequate margins is the treatment of choice for most cases. We report a case of urinary bladder pheochromocytoma with malignant clinical manifestation which required cystectomy.

references

  1. Deklerk DP, Catalona WJ, Nime FA, Freeman C: Malignant pheochromocytoma of the bladder: The late development of renal cell carcinoma. J Urol 1975, 113, 864-868.
  2. Heyman J, Cheung Y, Ghali V, Leiter E: Bladder pheochromocytoma: Evaluation with magnetic resonance imaging. J Urol 1989, 141, 1424-1426.
  3. Zornow DH, Bentrovato DA, Olson HW et al: Vesical-related paragangliomas. J Urol 1977, 118, 247-250.
  4. Mahoney EM, Harrison JH: Malignant pheochromocytoma: clinical course and treatment. J Urol 1977, 118, 225-229.
  5. Jurincic C, Gasser A, Metz KA et al: Pheochromocytoma of the urinary bladder. Urol Int 1992, 48, 232-234.
  6. Ansari MS, Goel S, Durairajan LN, Seth A: Malignant paraganglioma of the urinary bladder. A case report. Int Urol Nephrol 2001, 33, 343-345.
  7. Baima C, Casetta G, Vella R, Tizzani A: Bladder pheochromocytoma: a 3-year follow-up after transurethral resection (TURBT). Urol Int 2000, 65, 176-178.

correspondence

Krzysztof Bar
Klinika Urologii AM
ul. Jaczewskiego 8
20-950 Lublin
tel. 081 72 44 794
kl.urol.lublin@interia.pl