PTU - Polskie Towarzystwo Urologiczne
list of articles:

Management of congenital megalourethra
Article published in Urologia Polska 2006/59/1.

authors

Wiesław Urbanowicz, Radosław Mycek, Michał Wolnicki, Janusz Sulisławski
Klinika Urologii Dziecięcej Katedry Chirurgii Pediatrycznej Collegium Medicum Uniwersytetu Jagiellońskiego

keywords

children urinary tract, scaphoid megalourethra, fusiform megalourethra

summary

Introduction. Megalourethra is a primary, nonobstructive urethral dilatation. It is a very rare disorder characterised by the congenital absence of the corpus spongiosum and/or corpus cavernosum. Megalourethra has two varieties: scaphoid and fusiform. The defect may be an isolated event or else, as it is frequently the case, it is associated with prune-belly syndrome and other upper tract abnormalities.
The aim of the study. The report presents the diagnostic and therapeutic management of a patient with congenital scaphoid megalourethra.
Material and method. The patient was diagnosed radiologically (urography, cystography, urethrography) and had urethroscopy and cystoscopy performed. The deformation of the penis, glandular hypospadiasis and paradox urine incontinence were conspicuous. As a 5 year old boy, the patient was operated on while 5 years old and an urethroplasty was performed.
Results. The result of cosmetic penis operation was good. The patient needed about 6-week catheterisation after the operation because of difficulties in spontaneous urination.

references

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correspondence

Wiesław Urbanowicz
Klinika Urologii Dziecięcej
ul. Wielicka 265
30-663 Kraków
tel. (012) 658 20 11 wew. 1590